产品详情 |
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Antigenic Specificity | SGSH |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human |
Isotype | n/a |
Format | purified |
Size | 400 µL |
Concentration | n/a |
Applications | Western Blot: 1:4000 |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | SGSH Polyclonal Antibody. SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. |
Immunogen | n/a |
Other Names | HSS, MPS3A, SFMD, N-sulphoglucosamine sulphohydrolase, heparan sulfate sulfatase, mucopolysaccharidosis type IIIA, sulfoglucosamine sulfamidase, sulphamidase |
Gene, Accession # | Entrez: 6448; Uniprot: P51688 |
Catalog # | PA5-26584 |
Price | |
Order / More Info | SGSH Antibody from INVITROGEN ANTIBODIES |
Product Specific References | n/a |
产品资料 |
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