| 产品详情 |
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| Antigenic Specificity | BCKDHB |
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| Clone | polyclonal |
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| Host Species | Rabbit |
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| Reactive Species | human |
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| Isotype | n/a |
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| Format | purified |
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| Size | 100 µl |
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| Concentration | n/a |
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| Applications | Immunohistochemistry: 1:20-1:50, Western Blot: 0.4 µg/mL |
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| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
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| Description | BCKDHB Polyclonal Antibody. Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. |
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| Immunogen | n/a |
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| Other Names | E1B, dJ279A18.1, 2-oxoisovalerate dehydrogenase beta subunit, 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, BCKDE1B, BCKDH E1-beta, E1b-beta subunit of the branched-chain complex, branched chain alpha-ketoacid dehydrogenase E1-beta subunit, branched-chain alpha-ke |
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| Gene, Accession # | Entrez: 594; Uniprot: P21953 |
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| Catalog # | PA5-56785 |
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| Price | |
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| Order / More Info | BCKDHB Antibody from INVITROGEN ANTIBODIES |
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| Product Specific References | n/a |
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