产品详情 |
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Antigenic Specificity | ASL |
Clone | OTI14C7 |
Host Species | Mouse |
Reactive Species | human |
Isotype | IgG1 |
Format | purified |
Size | 100 µl |
Concentration | n/a |
Applications | Western Blot: 1:2000 |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | ASL Monoclonal Antibody (OTI14C7). This gene encodes a member of the lyase 1 family. The encoded protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in this gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency. A nontranscribed pseudogene is also located on the long arm of chromosome 22. Alternatively spliced transcript variants encoding different isoforms have been described. |
Immunogen | n/a |
Other Names | ASAL, argininosuccinase, arginosuccinase |
Gene, Accession # | Entrez: 435; Uniprot: P04424 |
Catalog # | MA5-26708 |
Price | |
Order / More Info | ASL Antibody from INVITROGEN ANTIBODIES |
Product Specific References | n/a |
产品资料 |
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