| 产品详情 |
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| Product Name | 3-Hydroxyglutaric Acid |
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| Description | Purity >95%. Glutaryl-CoA dehydrogenase (GCDH) is a mitochondrial matrix protein that catalyzes the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and carbon dioxide in the catabolic pathways of lysine, hydroxylysine, and tryptophan metabolism. 3-Hydroxyglutaric acid is one of several metabolites produced when insufficient levels of GCDH are available. Urinary levels of 3-hydroxyglutaric acid are elevated during glutaric acidemia type 1, an autosomal recessive GCDH deficiency disorder that can lead to neurodegeneration if left untreated. 3-Hydroxyglutaric acid is used as a biomarker of GCDH deficiency. |
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| Size | n/a |
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| Concentration | n/a |
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| Applications | n/a |
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| Other Names | 3-hydroxy-pentanedioic acid, 2,4-Dideoxypentaric Acid, 3-HG, 3-Hydroxyglutarate, 3-Hydroxypentanedioic Acid, 3-OH-GA, -Beta-Hydroxyglutaric Acid |
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| Gene, Accession, CAS # | CAS: 638-18-6 |
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| Catalog # | LS-H6064 |
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| Price | |
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| Order / More Info | 3-Hydroxyglutaric Acid from LIFESPAN BIOSCIENCES INC. |
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| Product Specific References | n/a |
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