产品详情 |
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Antigenic Specificity | MTM1 |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human, mouse, rat |
Isotype | n/a |
Format | Cy3 conjugate |
Size | 100ul |
Concentration | 1ug/ul |
Applications | IF(IHC-P) |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | MTM1 Polyclonal Antibody, Cy3 Conjugated. • Target Background: X-linked recessive myotubular myopathy is a congenital muscular disease characterized by severe hypotonia and generalized muscle weakness that, in most cases, leads to early postnatal death. The gene responsible for myotubular myopathy MTM1 encodes a dual specificity phosphatase, named myotubularin, which is highly conserved through evolution. The gene for MTM1 is localized to a 300 kb critical region on human Xq128 between IDS and GRBRA3. Human MTM1, a 603 amino-acid protein, is mutated in myot |
Immunogen | KLH conjugated synthetic peptide derived from human MTM1/Myotubularin. Immunogen Range: 225-275/603 |
Other Names | CG2; CNM; KIAA4176; mKIAA4176; Mtm; Mtm1; MTM1_HUMAN; MTMX; Myotubular myopathy 1; Myotubularin; XLMTM. |
Gene, Accession # | Gene ID: 4534, SwissProt: Q13496 |
Catalog # | bs-9178R-Cy3 |
Price | |
Order / More Info | MTM1 Antibody from BIOSS ANTIBODIES |
Product Specific References | n/a |
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