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Product Name | Recombinant Rat Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (Aldh4a1) |
Description | 24-563aa, Full Length of Mature Protein. MW: 61,869 Da. Purity >85% (SDS-PAGE). This protein belongs to the aldehyde dehydrogenase family of proteins. This enzyme is a mitochondrial matrix NAD-dependent dehydrogenase which catalyzes the second step of the proline degradation pathway, converting pyrroline-5-carboxylate to glutamate. Deficiency of this enzyme is associated with type II hyperprolinemia, an autosomal recessive disorder characterized by accumulation of delta-1-pyrroline-5-carboxylate |
Size | 0.05 mg (E-Coli), 0.05 mg (Baculovirus), 0.2 mg (E-Coli), 0.2 mg (Yeast), 0.05 mg (Mammalian-Cell) |
Concentration | n/a |
Applications | n/a |
Other Names | [Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial; Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial; aldehyde dehydrogenase 4 family, member A1; Aldehyde dehydrogenase family 4 member A1; L-glutamate gamma-semialdehyde dehydrogenase] |
Gene, Accession, CAS # | Aldh4a1, Gene ID: 641316, Accession: P0C2X9.1 |
Catalog # | MBS718856 |
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Order / More Info | Recombinant Rat Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (Aldh4a1) from MYBIOSOURCE INC. |
Product Specific References | n/a |
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